Extraskeletal Ewing's sarcoma, which occurs mainly in paravertebral region, lower extremity and retroperitoneum, is a rare primary malignant soft tissue tumor that has the same pathological characteristics of skeletal Ewing's sarcoma. Clear
histopathological separation from other round cell sarcoma, such as primitive rhabdomyosarcoma, neuroblatoma and neuroepithelioma, is oftern difficult without immunohistochemical staining.
We analysed clinical findings of five cases of extraskeletal Ewing's sarcoma that had been experienced from January 1987 to October 1991. All of the cases were diagnosed with immunohistochomical staining, including PAS and vimentin.
There were 3 females and 2 males, whose age was averaged as 19.8 years ranging from 1.8 to 36. Locations of the masses were proxiaml lower extremity in 2 cases, shoulder in one, pleural cavity in one, and submental triangle in one. Types of
treatment
were, wide excision with chemotheraphy and radiotherapy in two patients and wide excision with chemotherapy and radiotherapy in two patients and wide excision with chemotherapy in two. Only biopsy was performed in one patient who was lost in
follow-up.
The duration of follow-up except lost one, was average 27.8 months, and two of them died of disease. Lung metastasis was found in 3 cases, and one of them who showed metastasis at first visit, had remission after preoperative chemotherapy.
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